Double Outlet Right Ventricle
- The term double outlet right ventricle refers to a defect where both great arteries arise above the right ventricle.
- In most cases of double outlet right ventricle the great vessels are found lying side by side in a d-transposition configuration with the aorta on the right and pulmonary artery on the left.
- Rather than its own single anomaly, it is associated with other cardiac abnormalities. A ventricular septal defect is almost always present and 75% of patients have some degree of pulmonary stenosis. Transposition of the great, septal defects, or atrioventricular atresia, and a variety of valvular problems are also commonly seen with a double outlet right ventricle defect.
- The hemodynamics involved with double outlet right ventricle are dependent on the anatomy of the great vessels and associated defects. Decreased arterial oxygen saturation is almost always present but as a result of wide variation in anatomy, patients may or may not appear cyanotic and/or develop congestive heart failure, or be asymptomatic.
- Management of double outlet right ventricle depends on associated defects and the type of surgical correction they are amenable to.